Title: Long-term faithful recapitulation of transglutaminase 1-deficient lamellar ichthyosis in a skin-humanized mouse model, and insights from proteomic studies.
Authors: Aufenvenne, Karin; Rice, Robert H; Hausser, Ingrid; Oji, Vinzenz; Hennies, Hans Christian; Rio, Marcela Del; Traupe, Heiko; Larcher, Fernando
Published In J Invest Dermatol, (2012 Jul)
Abstract: Abstract not available from PubMed.
PubMed ID: 22437313
MeSH Terms: Animals; Disease Models, Animal*; Humans; Ichthyosis, Lamellar/etiology*; Ichthyosis, Lamellar/metabolism; Mice; Proteomics*; Transglutaminases/analysis; Transglutaminases/deficiency*; Transglutaminases/genetics; Transglutaminases/physiology